Segmental cutaneous hemangioma and spinal arteriovenous malformation (Cobb syndrome). Case report and historical perspective.
نویسندگان
چکیده
The discovery of either a dermatomal cutaneous nevus or a spinal arteriovenous malformation (AVM) should raise the suspicion of Cobb syndrome. The Cobb syndrome is a neurocutaneous syndrome in which there are metameric cutaneous and spinal AVMs. The authors present the case of a patient with acute cervical myelopathy and subtle cutaneous hemangiomas in whom a cervical perimedullary fistula was discovered. They also acknowledge Harvey Cushing's contribution to the recognition of this syndrome.
منابع مشابه
An Arteriovenous Malformation in the Suprapatellar Fat Pad of the Knee associated with Klippel-Trenaunay- Weber Syndrome: A Case Report
congenital disorder characterized by cutaneous hemangiomas, hypertrophy of bone and soft tissue, varicose veins, and clinically significant arteriovenous malformation (AVM) (1, 2, 3). AVMs associated with KTWS are located in the extremities, visceral organs, or spinal canal (1, 3). Most AVMs in the extremities are intramuscular or cutaneous. There is a paucity of data on AVMs in the suprapatell...
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ورودعنوان ژورنال:
- Journal of neurosurgery. Spine
دوره 3 3 شماره
صفحات -
تاریخ انتشار 2005